Marfan's Syndrome
Marfan’s syndrome is an inherited condition where there is a disorder affecting one of the components of connective tissue called fibrillin. It causes long, spidery fingers in a person with a high arched palate whose arm span is greater than their height. There may be associated cardiac abnormalities, and dislocation of the lens of the eye. This is an autosomal dominant condition - which means if you’ve got it, your offspring have a 50% chance of inheriting it. There is no treatment, but the presence of cardiac abnormalities may mean that antibiotics are required before surgical procedures - including dentistry - in order to prevent endocarditis (see disorders of the heart in the chest cavity section).
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